Harshe mai sauƙi
Menene Vein of Galen Malformation?
Tarin jijiyoyin jini ne a kwakwalwar jariri, a wurin da ya kamata a sami wani tantani mai laushi.
A cikin kwakwalwa mai lafiya, jini yana tafiya daga jijiyoyin arteri zuwa wani tantanin ƙananan jijiyoyi, sannan sai ya shiga jijiyoyin dawowa (veins). Wannan tantani yana rage saurin jini.
A cikin Vein of Galen Malformation, wannan tantani bai taɓa samuwa ba. Jijiyoyin arteri suna zubar da jini kai tsaye zuwa wata babbar jijiya mai zurfi a tsakiyar kwakwalwa, cikin cikakken matsin lamba. Jijiyar tana kumbura, kuma zuciya tana buƙatar yin aiki tuƙuru don ta iya jurewa.
Yana faruwa da wuri sosai a lokacin ɗaukar ciki, tun kafin kowa ya sani. Za ki kuma ga ana rubuta shi da VGAM, VGM, ko kuma "aneurysm of the vein of Galen". Duk suna nufin yanayi guda ɗaya.
Game da wannan bayani. Mun rubuta wannan cikin sauƙi daga majiyoyin likitanci da aka wallafa, kuma mun haɗa hanyar zuwa kowanne. Domin duk abin da ya shafi ɗanki musamman, likitocinki su ne masana.
Babu wani abu da kika yi da ya haifar da wannan
Daga Great Ormond Street Hospital: Vein of Galen Malformation ba wani abu ba ne da uwa ta yi ko ba ta yi ba a lokacin ɗaukar ciki da ya haifar da ita. Yawancin lokuta ba su da wani dalili da aka gano.
Ana iya yin maganinsa
Ana kiran jiyyar embolisation. Likita yana shigar da wani ƙaramin bututu ta cikin jijiyar jini, har zuwa kwakwalwa, ya toshe hanyoyin sadewa marasa kyau daga ciki. Ba a buɗe kwanyar kai ba. Yawanci ana yin ta a matakai, fiye da lokaci ɗaya.
Ana yin ta ne ta hannun interventional neuroradiologist. Ba su da yawa, kuma gogewa tana da matuƙar muhimmanci — wannan shine dalilin da ya sa neman ra'ayin wani likita a nan abu ne na kowa kuma mai hankali.
Abin da lambobi ke faɗa da gaske
Za ki sami ƙididdiga masu ban tsoro a intanet, da waɗanda ke kwantar da hankali. Dukansu gaskiya ne. Suna bayanin ƙungiyoyin yara daban-daban — kuma babu wanda ke gaya maki wanne. Don haka ga su, tare da ƙungiyoyin da suka shafa.
- Kusan kashi 6% sun mutu; kusan kashi 89% sun sami sakamako mai kyau — haɗaɗɗiyar nazari na marasa lafiya da aka yi wa jiyya na kowace shekaru, 2022–2024 (participant-level meta-analysis)
- Kusan kashi 40% sun mutu — kowane jariri da aka gano a Ingila cikin shekaru goma — ƙungiyar mafi tsananin rashin lafiya, an yi wa jiyya ko a'a (UK national cohort)
Jarirai da suka riga suka faɗa cikin gazawar zuciya sune mafi wahalar ƙungiya. Yara da aka gano kafin haihuwa, ko daga baya a jariranci, yawanci suna samun sakamako mafi kyau. Inda ɗanki yake tsaye, tambaya ce da kawai likitocinki za su iya amsawa.
Abin da dukan waɗannan lambobi suka yarda a kai: jiyya tana aiki, kuma yara masu wannan yanayi suna girma.
Kalmomin da za ki ji
- Embolisation
- Rufe hanyoyin sadewar jijiyoyin jini marasa kyau daga ciki, ta cikin wani ƙaramin bututu. Wannan ita ce jiyyar.
- Interventional neuroradiologist
- Ƙwararren likitan da ke yin ta. Ana kuma kiransa neuro-endovascular surgeon.
- Hydrocephalus
- Tarin ruwa a cikin kwakwalwa.
- Fontanelle
- Wurin taushi a kan kan jariri.
- Shunt
- Wani bututu da ke zubar da ruwa daga kwakwalwa. A wannan yanayi, ba shine mataki na farko yawanci ba.
- VGAM / VGM
- Wasu sunaye don ainihin abu ɗaya.
Inda za a karanta ƙari
Waɗannan su ne cibiyoyin da muke amincewa da su. Muna haɗa hanyar zuwa gare su maimakon sake rubuta bayaninsu.