Ulwimi olulula
Yintoni i-Vein of Galen Malformation?
Ngumsonto wemithambo-gazi engqondweni yosana, kwindawo ekwakumele kubekho uthungelwano olucekethekileyo.
Engqondweni esempilweni, igazi lihamba kwii-arteries liye kuthungelwano lwemithambo emincinci kakhulu, kuze kuthi ngoko lingene kwii-veins. Olo thungelwano luyalicothisa igazi.
Kwi-Vein of Galen Malformation, olo thungelwano alukhange lwenzeke. Ii-arteries zithulula ngqo kumthambo omkhulu ophakathi kwengqondo, ngengcindezi epheleleyo. Umthambo uyavuvukala, kwaye intliziyo kufuneka isebenze nzima kakhulu ukulandelisa.
Kwenzeka ekuqaleni kakhulu kokukhulelwa, kudala ngaphambi kokuba nabani na azi. Uya kukubona kubhalwa nangokuba yi-VGAM, i-VGM, okanye “i-aneurysm yomthambo we-Galen”. Zonke ezi yimeko enye kuphela.
Malunga nolu lwazi. Sikubhale oku ngolwimi olulula kusuka kwimithombo yezonyango epapashiweyo, kwaye sidibanisa nayo yonke. Nantoni na ekhethekileyo kumntwana wakho, oogqirha bakho ngabo abagunyazisiweyo.
Akukho nto oyenzileyo eyabangela oku
Ivela kwiGreat Ormond Street Hospital: i-Vein of Galen Malformation ayibangelwa yinto umama awayenzayo okanye awayingenziyo ngexesha lokukhulelwa. Uninzi lweemeko alunambangela iyaziwayo konke konke.
Iyanyangeka
Unyango yi-embolisation. Ugqirha udlulisa umbhobho ocekethekileyo ngomthambo-gazi, uye engqondweni, aze avale unxulumano olungaqhelekanga ngaphakathi. Ukhakhayi alukhange luvulwe. Ngesiqhelo kwenziwa ngamanyathelo, ngaphezu konyango olunye.
Yenziwa yi-interventional neuroradiologist. Ababaninzi, kwaye amava abaluleke kakhulu — yiyo loo nto ukucela enye imbono kule meko kuyinto eqhelekileyo nenengqiqo.
Oko amanani ngokwenene akutshoyo
Uya kufumana amanani oyikisayo kwi-intanethi, namanye athuthuzelayo. Omabini ayinyaniso. Achaza amaqela awohlukeneyo abantwana — kwaye phantse akukho namnye okuxelela ukuba nguwuphi. Ngoko ke nazi, namaqela awo edityaniswe nawo.
- Malunga ne-6% bafa; malunga ne-89% baba nesiphumo esihle — uhlalutyo oludityanisiweyo lwezigulane ezinyangiweyo zawo onke amaxesha obudala, 2022–2024 (uhlalutyo lwedatha yomthathi-nxaxheba ngamnye)
- Malunga ne-40% bafa — wonke usana olwabonakala e-UK kwiminyaka elishumi — elona qela ligula kakhulu, nokuba kwenziwe unyango kulo okanye akwenziwanga (uphando lwesizwe lwase-UK)
Iintsana esele zikwintlekele yentliziyo ziliqela elinzima ngakumbi. Iintsana ezifunyaniswa ngaphambi kokuzalwa, okanye kamva ebuntwaneni, ngesiqhelo zenza ngcono. Apho ikhona eyakho ingane ngumbuzo oogqirha bakho bodwa abanokuwuphendula.
Oko onke la manani avumelana ngako: unyango luyasebenza, kwaye abantwana abanale meko bayakhula.
Amagama oza kuwaphulaphula
- Embolisation
- Ukuvala imithambo-gazi engaqhelekanga ngaphakathi, ngombhobho ocekethekileyo. Lolu nyango.
- Interventional neuroradiologist
- Ingcali eyenza oku. Ibizwa nangokuba ngumhlinzi wemithambo-gazi yengqondo (neuro-endovascular surgeon).
- Hydrocephalus
- Ukukhukhuleka komswakama ngaphakathi engqondweni.
- Fontanelle
- Indawo ethambileyo entlokweni yosana.
- Shunt
- Umbhobho okhupha umswakama engqondweni. Kule meko ngesiqhelo asililo inyathelo lokuqala.
- VGAM / VGM
- Amanye amagama enye kanye into.
Apho ungafunda ngakumbi
La ngamaziko esiwathembayo. Sidibanisa nawo kunokuba siwabhale ngokutsha.