Kodokotela
I-Vein of Galen Malformation
Kungenzeka ungaze wabona nelilodwa icala. Uma wenza kanjalo, cishe kuzoba ingane esanda kuzalwa egula kakhulu kunazo zonke evikini lakho, futhi ukutholakala kwesifo akucaci. Leli khasi yilokho ebesifisa ukuthi udokotela owabona indodakazi yethu ubenikwe khona.
Mayelana naleli khasi. Yonke isitatimende sezokwelapha lapha sisusela emibhalweni eshicilelwe futhi ehloziwe ontanga, futhi sinye ngasinye sixhumanisa emthonjeni waso ngezansi. Kubhalelwe ukukusiza uqonde i-Vein of Galen Malformation uyidlulisele — hhayi ukungenela isibonelo sokuhlolwa ngongcweti.
Nini okufanele uyisole
Ukwehluleka kwenhliziyo okungachazwa (high-output cardiac failure) engane esanda kuzalwa
Nenhliziyo enesakhiwo esijwayelekile. Lokhu ukuvela okuvamile futhi ngokuvamile kuphuthelwa njengesifo senhliziyo osazalwa naso.
Umsindo wekhanda (cranial bruit)
Lalela nge-stethoscope kwi-fontanelle engaphambili nasemehlweni. Akubizi lutho futhi kuvame ukuba ukutholakala okuvula icala.
Ubukhulu bekhanda budlula amazinga ajwayelekile
Ikhanda elikhulu ngokweqile (macrocephaly) kunawo noma kungekho i-hydrocephalus ebonakalayo, engane.
I-fontanelle evuvukele noma eqinile
Nemithambo yesikhumba sekhanda nobuso egqamile futhi ivulekile kakhulu.
Ukubambezeleka kokukhula noma izithuthwane engane esikhulu kancane
Nekhanda elikhulu. Labo abavela sekwephuze yibo i-India ebashiyayo.
Yini okufanele uyithwebule
I-ultrasound yekhanda ene-Colour Doppler edlula kwi-fontanelle engaphambili ngokuvamile izokubonisa, futhi iyatholakala cishe yonke indawo. Kuwuhlolo lokuqala olunengqondo kunoma iyiphi ingane esanda kuzalwa enokwehluleka kwenhliziyo okungachazwa kanye ne-echo ejwayelekile.
I-MRI ene-MR angiography iyakuchaza kahle. I-catheter angiography yenziwa ithimba le-interventional njengengxenye yokuhlela ukwelashwa — akulona uhlolo lokuhlungela isifo.
Lapho ongadlulisela khona
Lokhu kwelashwa nge-endovascular embolisation, ngokuvamile ngezigaba, udokotela we-interventional neuroradiology noma udokotela we-neuro-endovascular surgery. Akulona ukuhlinzwa okuvulekile, futhi akulona icala lohlu lokuhlinzwa ubuchopho olujwayelekile.
Sifaka isikhungo ohlwini kuphela ngemva kokuqinisekisa ngocingo nomnyango ngokwawo — udokotela oqondile ophethe, inombolo eqondile yomnyango, indlela yokudlulisa, kanye nosuku esaqinisekisa ngalo okokugcina.
Lelo yizinga eliphakeme ngamabomu, futhi siyalibambelela: asishicileli igama lesibhedlela size sikhulume nalowo mnyango thina uqobo. Uma unengane phambi kwakho khona manje, sithumele umlayezo noma uthumele i-imeyili ku-contact@vogmindiafoundation.org futhi sizokutshela esikwaziyo.
Uma ulapha lesi simo
Singathanda ukuzwa kuwe, futhi singathanda ukukufaka ohlwini. Siyisikhungo esiqhutshwa abazali, hhayi ibhizinisi lokudlulisa iziguli — asithathi mali kumuntu, futhi asinabo ubudlelwane bebhizinisi nanoma yisiphi isibhedlela.
Singathanda futhi ukwazi okuthile akekho e-India okwaziyo okwamanje: ukuthi zingaki izingane ezinalesi simo. Alukho uhlu lwase-India, ayikho inombolo yokwanda kwesifo, futhi alukho ulwazi lwendlela isifo esiqhubeka ngayo. Uma usuke wawelapha amacala, singathanda kakhulu ukukhuluma.
Imithombo
- Berenstein A, Paramasivam S, et al. Vein of Galen Aneurysmal Malformation: Advances in Management and Endovascular Treatment. Neurosurgery, 2019.
- Paramasivam S. Hydrocephalus in Vein of Galen Malformations. Neurology India, 2021.
- Lecce F, et al. UK national cohort of neonatal vein of Galen malformation, 2006–2016.
- Great Ormond Street Hospital — Vein of Galen malformation