ᱰᱟᱠᱴᱚᱨ ᱠᱳᱣᱟᱜ ᱞᱟᱹᱜᱤᱫ
ᱣᱮᱱ ᱳᱯᱷ ᱜᱮᱞᱮᱱ ᱢᱟᱞᱯᱷᱚᱨᱢᱮᱥᱚᱱ
ᱟᱢ ᱡᱟᱡᱤᱢ ᱱᱚᱶᱟ ᱵᱟᱭ ᱧᱮᱞ ᱫᱟᱲᱮᱭᱟᱢ᱾ ᱡᱟᱦᱟᱸᱠᱷᱟᱱ ᱧᱮᱞᱟᱢ, ᱮᱱᱟ ᱟᱢᱟᱜ ᱦᱟᱯᱛᱟ ᱨᱮᱭᱟᱜ ᱡᱳᱛᱚ ᱴᱷᱮᱸ ᱵᱮᱢᱟᱨ ᱱᱳᱱᱮᱴ (neonate) ᱦᱩᱭᱩᱜᱟ, ᱟᱨ ᱵᱟᱛᱟᱣ ᱫᱚ ᱥᱩᱛᱟᱹᱨ ᱛᱮ ᱵᱟᱭ ᱩᱫᱩᱜᱚᱜᱟ᱾ ᱱᱚᱶᱟ ᱥᱟᱦᱴᱟ ᱫᱚ ᱟᱞᱮ ᱢᱮᱱᱛᱮᱭᱟ ᱡᱮ ᱟᱞᱮᱭᱟᱜ ᱠᱩᱲᱤ ᱦᱚᱯᱚᱱ ᱧᱮᱞ ᱠᱟᱛᱮ ᱰᱟᱠᱴᱚᱨ ᱴᱷᱮᱸ ᱮᱴᱟᱠᱚ ᱮᱢᱛᱟᱦᱮᱸᱸᱟᱭᱟᱜ ᱛᱟᱦᱮᱸᱠᱟᱱᱟ᱾
ᱱᱚᱶᱟ ᱥᱟᱦᱴᱟ ᱵᱟᱵᱚᱛ᱾ ᱱᱚᱸᱰᱮ ᱡᱚᱛᱚ ᱰᱟᱠᱴᱚᱨᱤ ᱠᱟᱛᱷᱟ ᱫᱚ ᱛᱚᱭᱳᱨ ᱦᱩᱭ ᱠᱟᱱ, ᱪᱤᱛᱷᱟᱹᱨ ᱨᱮ ᱚᱞ ᱟᱠᱟᱱ ᱠᱷᱚᱵᱚᱨ ᱠᱷᱚᱱ ᱧᱟᱢ ᱟᱠᱟᱱᱟ, ᱟᱨ ᱡᱚᱛᱚᱭ ᱛᱟᱞᱟ ᱨᱮᱭᱟᱜ ᱩᱛᱟᱹᱨ ᱛᱮ ᱡᱩᱲᱟᱶ ᱮᱫᱟ᱾ ᱱᱚᱶᱟ ᱫᱚ ᱣᱮᱱ ᱳᱯᱷ ᱜᱮᱞᱮᱱ ᱢᱟᱞᱯᱷᱚᱨᱢᱮᱥᱚᱱ ᱪᱤᱱᱦᱟᱹ ᱟᱨ ᱨᱮᱯᱷᱚᱨ ᱞᱟᱹᱜᱤᱫ ᱚᱞ ᱟᱠᱟᱱᱟ — ᱵᱤᱥᱮᱥᱚᱡ ᱰᱟᱠᱴᱚᱨ ᱨᱮᱭᱟᱜ ᱡᱚᱛᱚᱨ ᱨᱮᱭᱟᱜ ᱵᱚᱫᱚᱞ ᱵᱟᱭ ᱠᱟᱱᱟ᱾
ᱚᱠᱟ ᱚᱠᱛᱚ ᱥᱚᱸᱫᱮᱦ ᱢᱮ
ᱱᱳᱱᱮᱴ (neonate) ᱨᱮ ᱵᱟᱭ ᱚᱰᱚᱠ ᱠᱟᱱ ᱦᱟᱭ-ᱟᱩᱴᱯᱩᱴ ᱠᱟᱨᱰᱤᱭᱟᱠ ᱯᱮᱞᱭᱟᱨ (high-output cardiac failure)
ᱵᱮᱥ ᱵᱚᱱᱟᱶ ᱠᱟᱞᱡᱟ ᱥᱟᱶᱛᱮ᱾ ᱱᱚᱶᱟ ᱫᱚ ᱠᱞᱟᱥᱤᱠ ᱯᱨᱮᱡᱮᱸᱴᱮᱥᱚᱱ ᱠᱟᱱᱟ ᱟᱨ ᱡᱚᱛᱚ ᱴᱷᱮᱸ ᱡᱚᱱᱚᱢ ᱛᱮ ᱛᱟᱦᱮᱸᱸᱠᱟᱱ ᱠᱟᱞᱡᱟ ᱵᱤᱢᱟᱨ ᱠᱟᱛᱮ ᱵᱮᱰᱚᱸᱜ ᱟᱠᱟᱱᱟ᱾
ᱠᱨᱮᱱᱤᱭᱟᱞ ᱵᱨᱩᱭᱴ (cranial bruit)
ᱯᱩᱭᱞᱩ ᱯᱷᱚᱱᱴᱟᱱᱮᱞ ᱟᱨ ᱢᱚᱸᱫ ᱠᱚᱴᱚᱨ (orbit) ᱠᱳ ᱨᱮ ᱥᱴᱮᱛᱷᱳᱥᱠᱳᱯ ᱛᱟᱦᱮᱸᱸ ᱢᱮ᱾ ᱴᱟᱠᱟ ᱵᱟᱭ ᱟᱸᱜᱩᱪᱟᱭ ᱟᱨ ᱡᱟᱡᱤᱢ ᱴᱮᱴᱮ ᱱᱚᱶᱟ ᱴᱷᱮᱱ ᱴᱷᱮᱱ ᱵᱤᱢᱟᱨ ᱩᱫᱩᱜ ᱢᱮ ᱠᱟᱴᱷᱤᱱ ᱠᱟᱱᱟ᱾
ᱵᱚᱦᱚᱠ ᱨᱮᱭᱟᱜ ᱢᱟᱯ ᱥᱮᱸᱴᱟᱭᱤᱞ (centile) ᱛᱟᱨᱚᱶ ᱛᱟᱨᱚᱶ ᱠᱟᱡ ᱠᱟᱛᱮ ᱵᱟᱲᱟᱭᱟ
ᱢᱟᱠᱨᱳᱥᱮᱯᱷᱟᱞᱤ (macrocephaly), ᱦᱟᱭᱰᱳᱨᱳᱥᱮᱯᱷᱟᱞᱚᱥ ᱛᱟᱦᱮᱸᱸᱠᱟᱱ ᱟᱨᱦᱚᱸ ᱵᱟᱭ ᱛᱟᱦᱮᱸᱸᱠᱟᱱ, ᱦᱚᱯᱚᱱ ᱨᱮ᱾
ᱯᱷᱩᱞ ᱟᱨᱦᱚᱸ ᱠᱚᱸᱫ ᱟᱠᱟᱱ ᱯᱷᱚᱱᱴᱟᱱᱮᱞ
ᱵᱚᱦᱚᱠ ᱟᱨ ᱢᱩᱛᱟ ᱨᱮᱭᱟᱜ ᱯᱷᱩᱞ ᱟᱨ ᱦᱚᱲᱴᱟ ᱦᱟᱹᱭ ᱱᱟᱲᱤ ᱥᱟᱶᱛᱮ᱾
ᱢᱟᱨᱟᱝ ᱦᱚᱯᱚᱱ ᱨᱮ ᱵᱟᱲᱟᱣ ᱨᱮ ᱨᱟᱠᱟᱵ ᱟᱨᱦᱚᱸ ᱫᱚᱲᱟ
ᱢᱟᱨᱟᱝ ᱵᱚᱦᱚᱠ ᱥᱟᱶᱛᱮ᱾ ᱛᱟᱭᱚᱢ ᱛᱮ ᱩᱫᱩᱜ ᱟᱠᱟᱱ ᱠᱚ ᱫᱚ ᱡᱟᱦᱟᱸ ᱵᱷᱟᱨᱚᱛ ᱪᱩᱠᱚᱣᱟᱜᱟ ᱚᱱᱠᱩ ᱠᱟᱱᱟᱠᱚ᱾
ᱚᱠᱟ ᱤᱢᱮᱡ (image) ᱦᱮᱡ
ᱯᱩᱭᱞᱩ ᱯᱷᱚᱱᱴᱟᱱᱮᱞ ᱴᱷᱮᱸ ᱠᱚᱞᱚᱨ ᱰᱳᱯᱞᱚᱨ (colour Doppler) ᱥᱟᱶᱛᱮ ᱠᱨᱮᱱᱤᱭᱟᱞ ᱟᱞᱴᱨᱟᱥᱟᱩᱱᱰ (cranial ultrasound) ᱫᱚ ᱥᱟᱫᱷᱟᱨᱚᱱ ᱛᱮ ᱱᱚᱶᱟ ᱩᱫᱩᱜ ᱮᱫᱟ, ᱟᱨ ᱮᱱᱟ ᱫᱚ ᱡᱳᱛᱚ ᱡᱟᱭᱜᱟ ᱨᱮ ᱢᱮᱱᱟᱜᱟ᱾ ᱵᱟᱭ ᱚᱰᱚᱠ ᱠᱟᱱ ᱠᱟᱨᱰᱤᱭᱟᱠ ᱯᱮᱞᱭᱟᱨ ᱟᱨ ᱵᱮᱥ ᱤᱠᱚ (echo) ᱛᱟᱦᱮᱸᱸᱠᱟᱱ ᱡᱳᱛᱚ ᱱᱳᱱᱮᱴ ᱨᱮ ᱮᱱᱟ ᱫᱚ ᱢᱤᱫ ᱵᱩᱡᱷᱟᱹᱣ ᱯᱩᱭᱞᱩ ᱴᱮᱥᱴ ᱠᱟᱱᱟ᱾
MRI ᱟᱨ MR ᱮᱱᱡᱤᱳᱜᱨᱟᱯᱷᱤ (MR angiography) ᱫᱚ ᱮᱱᱟ ᱴᱷᱤᱠ ᱛᱮ ᱩᱫᱩᱜ ᱮᱫᱟ᱾ ᱠᱟᱛᱷᱮᱴᱚᱨ ᱮᱱᱡᱤᱳᱜᱨᱟᱯᱷᱤ (catheter angiography) ᱫᱚ ᱤᱱᱴᱚᱨᱵᱮᱱᱥᱚᱱᱚᱞ ᱴᱤᱢ ᱛᱮ ᱤᱞᱟᱡ ᱦᱮᱡ ᱦᱟᱹᱛᱟᱣ ᱨᱮᱭᱟᱜ ᱢᱤᱫ ᱦᱟᱹᱴᱤ ᱛᱮ ᱠᱟᱹᱢᱤ ᱦᱩᱭᱩᱜᱟ — ᱮᱱᱟ ᱫᱚ ᱥᱠᱨᱤᱱᱤᱝ (screening) ᱴᱮᱥᱴ ᱵᱟᱝ ᱠᱟᱱᱟ᱾
ᱚᱠᱟ ᱛᱮ ᱨᱮᱯᱷᱚᱨ ᱢᱮ
ᱱᱚᱶᱟ ᱫᱚ ᱮᱱᱰᱳᱣᱟᱥᱠᱩᱞᱟᱨ ᱮᱢᱵᱚᱞᱟᱭᱡᱮᱥᱚᱱ (endovascular embolisation) ᱛᱮ ᱤᱞᱟᱡ ᱦᱩᱭᱩᱜᱟ, ᱥᱟᱫᱷᱟᱨᱚᱱ ᱛᱮ ᱴᱷᱟᱶ ᱴᱷᱟᱶ ᱛᱮ, ᱢᱤᱫ ᱤᱱᱴᱚᱨᱵᱮᱱᱥᱚᱱᱚᱞ ᱱᱤᱣᱨᱳᱨᱮᱰᱤᱭᱳᱞᱚᱡᱤᱥᱴ ᱟᱨᱦᱚᱸ ᱱᱤᱣᱨᱳ-ᱮᱱᱰᱳᱣᱟᱥᱠᱩᱞᱟᱨ ᱥᱚᱨᱡᱚᱱ ᱛᱮ᱾ ᱮᱱᱟ ᱳᱯᱮᱱ ᱥᱚᱨᱡᱚᱨᱤ (open surgery) ᱵᱟᱝ ᱠᱟᱱᱟ, ᱟᱨ ᱥᱟᱫᱷᱟᱨᱚᱱ ᱱᱤᱣᱨᱳᱥᱚᱨᱡᱤᱠᱟᱞ (neurosurgical) ᱞᱤᱥᱴᱤ ᱨᱮᱭᱟᱜ ᱠᱮᱥ ᱵᱟᱝ ᱠᱟᱱᱟ᱾
ᱟᱞᱮ ᱢᱤᱫ ᱠᱮᱱᱫᱨᱟ ᱨᱮᱭᱟᱜ ᱧᱩᱛᱩᱢ ᱚᱱᱟᱡ ᱛᱟᱭᱚᱢ ᱛᱮ ᱛᱩᱞᱟ ᱠᱟᱛᱮ ᱚᱰᱟᱸᱰᱟᱜᱟᱞᱮ ᱡᱟᱦᱟᱸ ᱴᱟᱲᱟᱝ ᱚᱱᱟ ᱵᱤᱵᱷᱟᱜ ᱥᱟᱶᱛᱮ ᱯᱷᱚᱱ ᱛᱮ ᱛᱟᱭ ᱟᱠᱟᱫᱟᱞᱮ — ᱧᱩᱛᱩᱢ ᱟᱠᱟᱱ ᱠᱚᱸᱥᱟᱞᱴᱮᱸᱴ, ᱵᱤᱵᱷᱟᱜ ᱨᱮᱭᱟᱜ ᱰᱟᱭᱨᱮᱠᱴ ᱱᱚᱸᱵᱚᱨ, ᱨᱮᱯᱷᱚᱨᱟᱞ ᱨᱟᱥᱛᱟ, ᱟᱨ ᱟᱞᱮ ᱴᱤᱸᱜᱩ ᱛᱩᱞᱟ ᱟᱠᱟᱱ ᱛᱟᱨᱤᱠᱷ᱾
ᱮᱱᱟ ᱫᱚ ᱡᱟᱱᱵᱩᱡᱷᱟᱹᱣ ᱛᱮ ᱢᱟᱨᱟᱝ ᱴᱷᱤᱠ ᱠᱟᱱᱟ, ᱟᱨ ᱟᱞᱮ ᱚᱱᱟ ᱴᱟᱸᱲ ᱛᱮ ᱛᱟᱦᱮᱸᱠᱟᱱᱟᱞᱮ: ᱟᱞᱮ ᱟᱥᱯᱟᱛᱟᱞ ᱧᱩᱛᱩᱢ ᱵᱟᱭ ᱚᱞᱟᱞᱮ ᱡᱟᱸᱣᱟᱭ ᱟᱞᱮ ᱚᱱᱟ ᱵᱤᱵᱷᱟᱜ ᱥᱟᱶᱛᱮ ᱟᱞᱮ ᱠᱟᱛᱷᱟ ᱵᱟᱭ ᱦᱩᱭᱮᱱᱟ᱾ ᱡᱟᱦᱟᱸᱠᱷᱟᱱ ᱟᱢᱟᱜ ᱛᱟᱞᱟ ᱨᱮ ᱦᱚᱯᱚᱱ ᱢᱮᱱᱟᱜᱟ, ᱟᱞᱮ ᱠᱮ ᱠᱷᱚᱵᱚᱨ ᱮᱢ ᱢᱮ ᱟᱨᱦᱚᱸ contact@vogmindiafoundation.org ᱨᱮ ᱤᱢᱮᱞ ᱢᱮ, ᱟᱨ ᱟᱞᱮ ᱟᱞᱮ ᱛᱟᱦᱮᱸᱸ ᱠᱷᱚᱵᱚᱨ ᱵᱟᱛᱟᱶᱟᱞᱮ᱾
ᱡᱟᱦᱟᱸᱠᱷᱟᱱ ᱟᱢ ᱱᱚᱶᱟ ᱵᱤᱢᱟᱨ ᱨᱮᱭᱟᱜ ᱤᱞᱟᱡ ᱠᱟᱹᱢᱤᱭᱟᱢ
ᱟᱞᱮ ᱟᱢ ᱠᱷᱚᱱ ᱟᱭᱩᱢ ᱢᱮᱱᱛᱮᱭᱟᱞᱮ, ᱟᱨ ᱟᱞᱮ ᱟᱢᱟᱜ ᱧᱩᱛᱩᱢ ᱞᱤᱥᱴᱤ ᱨᱮ ᱛᱩᱞᱟ ᱢᱮᱱᱛᱮᱭᱟᱞᱮ᱾ ᱟᱞᱮ ᱫᱚ ᱦᱚᱲ-ᱮᱲᱟ ᱛᱮ ᱪᱟᱞᱟᱶ ᱟᱠᱟᱱ ᱯᱷᱟᱩᱸᱰᱮᱥᱚᱱ ᱠᱟᱱᱟᱞᱮ, ᱨᱮᱯᱷᱚᱨᱟᱞ ᱵᱤᱡᱱᱮᱥ ᱵᱟᱝ ᱠᱟᱱᱟᱞᱮ — ᱟᱞᱮ ᱚᱠᱚᱭ ᱛᱟᱭᱚᱢ ᱦᱚᱸ ᱯᱷᱤ ᱵᱟᱭ ᱧᱟᱢᱟᱞᱮ, ᱟᱨ ᱚᱠᱚᱭ ᱟᱥᱯᱟᱛᱟᱞ ᱥᱟᱶᱛᱮ ᱦᱚᱸ ᱠᱚᱢᱚᱨᱥᱤᱭᱟᱞ (commercial) ᱡᱩᱲᱟᱶ ᱵᱟᱭ ᱢᱮᱱᱟᱜᱟᱞᱮ᱾
ᱟᱞᱮ ᱮᱴᱟᱜ ᱠᱟᱛᱷᱟ ᱦᱚᱸ ᱟᱭᱩᱢ ᱢᱮᱱᱛᱮᱭᱟᱞᱮ ᱡᱟᱦᱟᱸ ᱵᱷᱟᱨᱚᱛ ᱨᱮ ᱚᱠᱚᱭ ᱦᱚᱸ ᱚᱰᱚᱠ ᱵᱟᱭ ᱵᱟᱰᱟᱭᱟ: ᱚᱠᱟ ᱴᱟᱨᱚᱢ ᱦᱚᱯᱚᱱ ᱠᱳ ᱱᱚᱶᱟ ᱵᱤᱢᱟᱨ ᱥᱟᱶᱛᱮ ᱢᱮᱱᱟᱜᱟᱠᱚ᱾ ᱵᱷᱟᱨᱚᱛ ᱨᱮ ᱨᱮᱡᱤᱥᱴᱨᱤ ᱵᱟᱝ ᱠᱟᱱᱟ, ᱤᱱᱥᱤᱰᱮᱸᱴ (incidence) ᱨᱮᱭᱟᱜ ᱟᱸᱠᱲᱟ ᱵᱟᱝ ᱢᱮᱱᱟᱜᱟ, ᱟᱨ ᱱᱟᱸᱪᱨᱟᱞ-ᱦᱤᱥᱴᱳᱨᱤ (natural-history) ᱰᱮᱴᱟ ᱦᱚᱸ ᱵᱟᱝ ᱢᱮᱱᱟᱜᱟ᱾ ᱡᱟᱦᱟᱸᱠᱷᱟᱱ ᱟᱢ ᱠᱮᱥ ᱠᱳ ᱤᱞᱟᱡ ᱟᱠᱟᱫᱟᱢ, ᱟᱞᱮ ᱰᱷᱮᱨ ᱠᱟᱛᱷᱟ ᱟᱭᱩᱢ ᱢᱮᱱᱛᱮᱭᱟᱞᱮ᱾
ᱥᱚᱨᱥᱚ ᱠᱳ
- Berenstein A, Paramasivam S, et al. Vein of Galen Aneurysmal Malformation: Advances in Management and Endovascular Treatment. Neurosurgery, 2019.
- Paramasivam S. Hydrocephalus in Vein of Galen Malformations. Neurology India, 2021.
- Lecce F, et al. UK national cohort of neonatal vein of Galen malformation, 2006–2016.
- Great Ormond Street Hospital — Vein of Galen malformation